Biotinidase
MESHD043523
An enzyme which catalyzes the release of BIOTIN from biocytin. In human, defects in the enzyme are the cause of the organic acidemia MULTIPLE CARBOXYLASE DEFICIENCY or BIOTINIDASE DEFICIENCY.
Synonyms
- Biocytin Hydrolase
- Hydrolase, Biocytin
Source last updated 2026-05-24T15:25:13.889Z