Argininosuccinate Synthase
MESHD001124
An enzyme of the urea cycle that catalyzes the formation of argininosuccinic acid from citrulline and aspartic acid in the presence of ATP. Absence or deficiency of this enzyme causes the metabolic disease CITRULLINEMIA in humans. EC 6.3.4.5.
Synonyms
- Synthase, Argininosuccinate
- Argininosuccinate Synthetase
- Synthetase, Argininosuccinate
Source last updated 2026-05-24T15:28:12.255Z