Argininosuccinate Lyase
MESHD001123
An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease ARGININOSUCCINIC ACIDURIA in man. EC 4.3.2.1.
Synonyms
- Lyase, Argininosuccinate
- Argininosuccinase
Source last updated 2026-05-24T15:28:12.255Z