iDrugBank

Atypical Hemolytic Uremic Syndrome

MESHD065766

An hereditary hemolytic uremic syndrome associated with variations in the gene that encodes COMPLEMENT FACTOR H, or the related proteins CFHR1 and CFHR3. Disease often progresses to CHRONIC KIDNEY FAILURE without the prodromal symptoms of ENTEROCOLITIS and DIARRHEA that characterize typical hemolytic uremic syndrome.

Synonyms

  • Atypical Hemolytic-Uremic Syndrome
  • Atypical Hemolytic-Uremic Syndromes
  • Hemolytic-Uremic Syndrome, Atypical
  • Hemolytic-Uremic Syndromes, Atypical
  • Syndrome, Atypical Hemolytic-Uremic
  • Syndromes, Atypical Hemolytic-Uremic
  • Non-Stx-Hus
  • Non Stx Hus
  • Hemolytic Uremic Syndrome, Atypical
  • Nonenteropathic HUS
  • HUS, Nonenteropathic
  • HUSs, Nonenteropathic
  • Nonenteropathic HUSs
  • Non-Shiga-Like Toxin-Associated HUS
  • HUS, Non-Shiga-Like Toxin-Associated
  • HUSs, Non-Shiga-Like Toxin-Associated
  • Non Shiga Like Toxin Associated HUS
  • Non-Shiga-Like Toxin-Associated HUSs
  • Toxin-Associated HUS, Non-Shiga-Like
  • Toxin-Associated HUSs, Non-Shiga-Like

Source last updated 2026-05-24T15:24:21.720Z