iDrugBank

Aspartylglucosaminuria

MESHD054880

A recessively inherited, progressive lysosomal storage disease caused by a deficiency of GLYCOSYLASPARAGINASE activity. The lack of this enzyme activity results in the accumulation of N-acetylglucosaminylasparagine (the linkage unit of asparagine-linked glycoproteins) in LYSOSOMES.

Synonyms

  • Aspartylglucosaminurias
  • Aspartylglycosaminuria
  • Aspartylglycosaminurias
  • Aspartylglucosamidase Deficiency
  • Aspartylglucosamidase Deficiencies
  • Deficiencies, Aspartylglucosamidase
  • Deficiency, Aspartylglucosamidase
  • AGA Deficiency
  • AGA Deficiencies
  • Deficiencies, AGA
  • Deficiency, AGA
  • Glycoasparaginase Deficiency
  • Deficiencies, Glycoasparaginase
  • Deficiency, Glycoasparaginase
  • Glycoasparaginase Deficiencies

Source last updated 2026-05-24T15:24:44.734Z