1-Pyrroline-5-Carboxylate Dehydrogenase
MESHD050842
An enzyme that catalyzes the oxidation of 1-pyrroline-5-carboxylate to L-GLUTAMATE in the presence of NAD. Defects in the enzyme are the cause of hyperprolinemia II.
Synonyms
- 1 Pyrroline 5 Carboxylate Dehydrogenase
- Dehydrogenase, 1-Pyrroline-5-Carboxylate
- GGS Dehydrogenase
- Dehydrogenase, GGS
- NADP+ Specific 8-Glutamate Semialdehyde Dehydrogenase
- NADP+ Specific 8 Glutamate Semialdehyde Dehydrogenase
- Delta(1)-Pyrroline-5-Carboxylate Dehydrogenase
- Glutamic-Gamma-Semialdehyde Dehydrogenase
- Dehydrogenase, Glutamic-Gamma-Semialdehyde
- Glutamic Gamma Semialdehyde Dehydrogenase
- Glutamyl-Gamma-Semialdehyde Dehydrogenase
- Dehydrogenase, Glutamyl-Gamma-Semialdehyde
- Glutamyl Gamma Semialdehyde Dehydrogenase
Source last updated 2026-05-24T15:25:04.520Z