Complement C1 Inhibitor Protein
MESHD050718
An endogenous 105-kDa plasma glycoprotein produced primarily by the LIVER and MONOCYTES. It inhibits a broad spectrum of proteases, including the COMPLEMENT C1R and the COMPLEMENT C1S proteases of the CLASSICAL COMPLEMENT PATHWAY, and the MANNOSE-BINDING PROTEIN-ASSOCIATED SERINE PROTEASES. C1-INH-deficient individuals suffer from HEREDITARY ANGIOEDEMA TYPES I AND II.
Synonyms
- C1 Esterase Inhibitor
- Esterase Inhibitor, C1
- C1-Inhibitor Protein
- C1 Inhibitor Protein
- C1-INH Protein
- C1 INH Protein
- Plasma Protease C1 Inhibitor
- Complement C1-Inhibitor Protein
- Serpin G1
- Serpin Family G Member 1
- SERPING1
Source last updated 2026-05-24T15:25:04.520Z