iDrugBank

Biotinidase Deficiency

MESHD028921

The late onset form of MULTIPLE CARBOXYLASE DEFICIENCY (deficiency of the activities of biotin-dependent enzymes propionyl-CoA carboxylase, methylcrotonyl-CoA carboxylase, and PYRUVATE CARBOXYLASE) due to a defect or deficiency in biotinidase which is essential for recycling BIOTIN.

Synonyms

  • Biotinidase Deficiencies
  • Deficiencies, Biotinidase
  • Deficiency, Biotinidase
  • Deficiency, Multiple Carboxylase, Late-Onset
  • Late-Onset Biotin-Responsive Multiple Carboxylase Deficiency
  • Late Onset Biotin Responsive Multiple Carboxylase Deficiency
  • Carboxylase Deficiency, Multiple, Late-Onset
  • Multiple Carboxylase Deficiency, Late-Onset
  • Multiple Carboxylase Deficiency, Late Onset
  • BTD Deficiency
  • BTD Deficiencies
  • Deficiencies, BTD
  • Deficiency, BTD
  • Late-Onset Multiple Carboxylase Deficiency
  • Late Onset Multiple Carboxylase Deficiency

Source last updated 2026-05-24T15:25:24.801Z