iDrugBank

Argininosuccinate Lyase

MESHD001123

An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease ARGININOSUCCINIC ACIDURIA in man. EC 4.3.2.1.

Synonyms

  • Lyase, Argininosuccinate
  • Argininosuccinase

Source last updated 2026-05-24T15:28:12.255Z